pierre robin sequence geographical differences

A velopharyngeal incompetency is further amplified in the presence of hypoplastic adenoidal tissue. Generally, it prevails that the wider the cleft and the shorter the sP, the more likely velopharyngeal incompetency will occur. In a few severe cases, dynamic sphincteroplasty or palatal distraction was performed.

Secondary reconstruction in Siebold–Robin sequence and Fairbairn–Robin triad patientsįor FRT patients, most secondary reconstructions due to velopharyngeal incompetency consisted of velopharyngeal flap procedures. This analysis is based on 266 Pierre Robin syndrome (PRS) cases which represent a part of an overall database of 4158 cleft cases recorded at the largest cleft lip and palate unit in South Africa. In many SRS cases, the infants might not have been referred to a cleft clinic seeing that they did not present with a palatal cleft, and may most probably have been successfully managed by pediatricians with long-term nasopharyngeal intubation treatment. In the database presented here, only a rather small group of cases has been detected and recorded. The number of SRS cases reported by a European clinic greatly contributes to the total number of cases reported in the literature.

Clear clinical distinctions have been elaborated between SRS and FRT in a total of 266 cases in a database of 4158 recorded cleft cases. Different clinical findings in these conditions lead to various custom-made treatments. This final part of the publication series discusses treatment strategies and modalities for patients suffering from Siebold–Robin sequence (SRS) and Fairbairn–Robin triad (FRT).

Pierre robin sequence geographical differences